Beware of Multiple (diffuse) Neuro/cerebral Cysticercosis

BEWARE OF MULTIPLE (DIFFUSED) NEURO /from International friends and as per the advice of Dr
CEREBRAL CYSTICERCOSIS----------------A LIFEAyub K. Ommayya, Neurosurgeon, Maryland, USA, I
THREATENING DISEASEhave taken her to Mexico City in the year 1986
This is a real life story of a brave girl who had notwhere the incidence of this disease is high. The
resigned to her fate despite affliction of an incurableAmerican Doctors have stated that they don't have
disease and lived on hope after hope. She hasmuch knowledge on the disease as it occurs only in
exhibited strong will power and determination tounderdeveloped countries due to unhygienic
overcome the pangs in life. She has withered manyconditions and lack of sanitation and said that
storms, displayed rare courage despite several oddsMexicans have greater awareness in the
and stood as a shining example to instill confidence inmanagement of the disease. The Nuclear Medicine
others passing through the same turmoil.Specialists in Mexico have claimed that they have
In the year 1977, my daughter when she was hardlydeveloped a vaccine for the extermination of not
7 years old, suddenly, complained of unbearableonly viable cysts but even the calcified cysts. I have
(splitting/hammering) headache, projectile vomitingscontacted Bhabha Atomic Research Centre,
that reminded me of the Hollywood horror movieTrombay, Mumbai for injectible form of I-131 and
"EXORCIST" . The pressure in the alimentary canalthey had expressed their inability to supply the same
built-up was so high, the vomit resembled the gushas it was available only for oral administration and
of a fountain. When there was no relief withrequired clearance to make it in injectible form from
conventional pain killers, anti-vomitants andnone other than Rajiv Gandhi, the then PM holding
dehydration had set in already, she was rushed to Drthe portfolio of Atomic Energy. Under these
Ram Manohar Lohia Hospital, Delhi and was put onextenuating circumstances, the Mexican Doctors have
drip. The Doctors could not make a prognosis withinvited us to go to their country as radio active
routine tests besides X-ray of skull. As such, she wasmaterial can't be supplied through diplomatic bag and
shifted to Gobind Ballabh Pant Hospital which wasmoreover its half life reported to be 8 days only.
better equipped to deal with Neurological andHowever, the treatment provided by Dr Gregario
Neurosurgical problems. In those days, India did notSkromne Kadulbik of Mexico has proved to be a tall
have sophisticated diagnostic tools like CAT SCAN /claim and it did not bring any improvement in her
MRI etc. In the absence of latest equipment, Dr A.case as they have used my daughter as a guinea pig
Krishna Reddy, M.S. M.Ch., a young and brilliantfor conducting experiments on her. On the other
Neurosurgeon had conducted "Carotid Angiogram"hand, she has developed hyperthyroidism due to
(where a dye is injected under general anaesthesiaintravenous administration of Iodine-131, a radio-active
through the carotid artery leading to the brain andsubstance used as a carrier to the vaccine to the
X-rays are taken in quick succession to know thebrain. Brig. N. Lakshmipathi, VSM, Director, Institute of
presence of benign or malignant tumour) andNuclear Medicine & Allied Sciences, Government of
"Pneumo-Encephalogram" (which was again a tortuousIndia, Delhi has expressed his inability for administering
process-pumping pressurised air through24 booster doses provided by Dr Skromne as the
inter-vertebrae) but nothing abnormal could beNuclear Medicine Committee of BARC has expressed
detected. However, on close examination, he hadtheir inability to endorse the proposed treatment. The
found with the aid of an opthalmoscope, bilateral-Radiologist at the Mexican Hospital has exclaimed that
papilodema and intra-cranial tension (ICT) which wereshe has not seen before so many cysts scattered all
serious symptoms indicative that something had goneover in a single brain. Some of the Professors of
wrong in the brain. To rule out the possibility of BrainMedical Colleges in India desired to have the cat scan
T.B., a full course of antibiotic injections were alsopictures for teaching purpose. Based on the cat scan,
given. He has given a provisional diagnosis asa Doctor in India has submitted dissertation for the
"Cerebral Cysticercosis" and prescribedaward of a Ph.D. Despite her ill health and countless
"cortico-steroid" (which is usually prescribed by theepileptic attacks, she is intelligent and highly educated
Doctors as a last resort that serves as a maskingbut is having amnesia (forgetful nature of losing key
effect/camouflage- to suppress the symptoms onlybunch, purse etc. but elephantine memory of
but will not tackle the root cause of the disease) soinstances of the past.) However, she is unable to lead
as to reduce the ICT and give immediate relief toan active life due to heavy medication and requires
the patient and liberal quantities of Glycerineminimum 9-10 hrs sleep. In the event of an impending
(pharmaceutical preparation) and 'Decadron' (a steroidepileptic attack, she is given 'Diazepam' 2 cc
) injection as SOS. Glycerine has a unique feature ofIntra-venous to lull her into sleep. She is now 40 year
unhindered entry into the brain and is supposed toold and is blessed with a normal, intelligent and
absorb waste fluids accumulated in the brain. Shebeautiful female baby 4 years back through a
used to make tantrums to take glycerine althoughcaesarean section despite innumerable problems like
sweet in taste but is sticky like a glue.. Afterstatic epilepsy during pregnancy (in Vitro)
sometime she was discharged from the Hospital. Wenecessitating hospitalization a couple of times. Unlike
have then approached Dr P.N. Tandon, Head ofmost greedy and money minded Indian Doctors, to
Neurosurgery,AIIMS who was then credited with theher good luck, at last, she found an excellent doctor
highest number of successful brain operations in India.couple, husband a Neurologist and wife a
He was also very much puzzled and referred to DrGynaecologist- a perfect combination ( Jain Nursing
Kuchi Pillai, Endocrinologist with the observation-- "TheHome, Preet Vihar, Delhi) who had taken
child is a baffling problem who at one time hadextraordinary care of her throughout the pregnancy.
evidence of raised I.C.P. for which all investigationsWe have tried Homoeopathy as an alternative
have proved of no avail (Angio, PEG, EMI scan). Shemedicine with disastrous results. In her case,
is now totally dependent on Cortisone. Is there anyNeurosurgeons have clearly told that anti-convulsants
way of solving her problem?" Soon after dischargecan't be discontinued under any circumstances that
from the hospital, she has started getting convulsionsmight expose her life to mortality. According to
seizures with high temperature for unknown reasonsmedical sources, any damage done to the brain is
and she was again hospitalized, this time, inirrepairable as the cysts lodged in the brain shall
Safdarjung Hospital, New Delhi when Dr Maheswari,remain active for nearly 7 years and later they are
eminent Neurologist has carried outcalcified forming lesions/permanent scars on the brain
"Electro-Encephalogram" and confirmed sudden burstsurface. The cysts even after calcification produce
of waves in the graph in the parieto-occipital regionelectrical discharges triggering epileptic fits. If the
of the brain and confirmed epileptic condition andpresence of cysts are limited to one or two, they
prescribed anti-convulsants and wide spectrumcan be removed by operating the brain depending on
anti-biotic (Septran). Due to continuous damage beingtheir location and accessibility. In many cases, these
done by the cortisone, the same was graduallycysts are lodged in urinary bladder, eyes or in any
tapered under the cover of Adrino-cortico-tropicalother part of the human body but the problem arises
Hormone injections imported from U.K. and it waswhen cysts are lodged in the brain as they can make
finally dispensed with. It is less said than better aboutentry only into the brain but have no exit point. The
the drug withdrawal symptoms experienced whichseriousness of the patient can be gauzed from the
were more serious than the disease itself. In thefact that a lady in her early thirties, wife of an
mean time, the first "Cat Scan" machine was acquiredArmed Forces Officer who was under treatment
by the All India Institute of Medical Sciences (AIIMS)along with my daughter had committed suicide unable
in New Delhi in April, 1979 and the scan taken in theto bear the suffering. Despite her protracted illness,
first instance has revealed nothing abnormal (NAD)she has shown brevity in adversity and with single
and we were overjoyed to learn about it. But, ourminded devotion pursued her studies in Delhi
happiness was short-lived as Dr Ivaturi Meera Devi,University - B.A.(Hons) English Litt., M.A. and B.Ed with
Radiologist repeated the test when countless cystsflying colours. It is very sad that a carefree life of
of the tapeworm scattered all over the brain werechildhood to be spent in merriment was robbed off
clearly visible and confirmed the diagnosis as "multiplefrom her due to protracted illness. Whenever,
(diffused) cerebral cisticercosis" for which there wasindications of an impending seizure are noticed, she is
no remedy those days and the patient had toadministered "Diazepam" 2 cc I.V. injection. The Delhi
depend on anti-convulsants to be supplemented byUniversity was very co-operative and provided extra
Vitamin-D for the rest of life with its inevitable sidetime for answering each question paper on the basis
effects like gingivitis (loose gums), behavioralof a medical certificate issued by the Head of
changes, progressive loss of memory andNeurosurgery Deptt. and University Doctor as with
osteoporosis.each epileptic attack, she needed physiotherapy to
We did not have the slightest idea that it wasregain the normal function of her limbs. Marriage is a
symptomatic of a strange and incurable diseasetaboo especially for women suffering from epilepsy in
caused by eating tapeworm (Taenia solium.) infectedIndian Society. Very recently only, the draconian law
cole vegetable crops like carrot, radish, beet root,has been amended by the Indian Parliament annulling
cabbage and cauliflower grown in unhealthy bogs (the law of equating the epilepsy as lunacy and
grown under sewage water) although the disease isallowing divorce. However, a broadminded, highly
common in pork eaters when it was not properlyqualified and affluent financial wizard of 33 years has
cooked. Pigs are the alternate hosts of tapewormmarried her when she had attained the age of 30
parasite. Although, we are pure vegetarians, myyears and her medical history was not hidden from
daughter is afflicted with this infection .him.
As the attending Neurosurgeon who was takingI was in touch with various multinational
special interest in the patient joined the Nationalpharmaceutical companies like Bayer and E-Merck
Institute of Mental Health & Neurosciences, I have(Germany) engaged in evolving medicines for
admitted my daughter in NIMS in Bangalore as hercysticercosis even before they have undertaken the
condition had deteriorated. Despite religious intake ofclinical trials. Eventually, E-Merck has developed a
anti-epileptic medicines in the recommended dosages,medicine of choice 'praziquantel' in the form of tablets
she used to get seizures off and on sometimes mildcosting full course around Rs.3,000/- which is said to
and sometimes in severe form. Sometimes withbe highly efficacious in the initial stages of infection.
forewarning like flashes in the eyes, slight headache,The medicine is to be administered under the close
flickering of eye lids, disorientation, hallucinations,supervision of a Neurologist or a Neurosurgeon only
incoherent speech, tremors, (generalized convulsions)to handle the fluctuations in the Intra-cranial pressure.
and sometimes all of a sudden, she used to fall down.However, there is no hope for the old patients
Dr G.N. Narayana Reddy, Director, NIMS opined onafflicted with this dreadful disease when the cysts
09th Nov. 1979 that there was no treatment availableare already calcified in the brain as the medicine won't
for cysticercosis in the brain. He had no knowledge ofwork.
any indigenous system of medicine which could helpThe incidence of the disease has been reported to
in such a condition. The type and extent of damagebe high in the Union Territory of Chandigarh according
done depends very much on the site of the lesionto an independent survey conducted and reported in
and the reaction of the brain to the cysticercosis.print media as a number of cases have been
They may remain silent without producing symptomsreported by the Post Graduate Institute of Medical
for a long time but suddenly, they may produceSciences there. Medical Extension services of various
symptoms of varying nature according to him. Asstates and Union Govt. should play a prominent and
Neurosurgery facilities in Chennai were considered farkey role in educating the general public with an
better in those days, I have taken her to Chennaiaggressive publicity drive about the danger in store
and was treated there for 2 years (1980-82) underfor them especially in the consumption of "SALAD"
the expert supervision of Drs B. Ramamurthy and S.and Vegetables without proper washing and thorough
Kalyanaraman in the General Hospital there. With helprinsing in filtered water.