What Research Is Being Done?

Investigators from many fields of medicine and healthpreterm infants who will develop cerebral palsy. If
are using their expertise to help improve thethese screening techniques are successful, doctors
treatment and diagnosis of cerebral palsy. Much ofwill be able to identify infants at risk for cerebral
their work is supported through the NINDS, thepalsy before they are born.
National Institute of Child Health and HumanNoninvasive methods to record the brain activity of
Development (NICHD), other agencies within theunborn babies in the womb and to identify those with
federal government, nonprofit groups such as thebrain damage or abnormalities would also be a
United Cerebral Palsy Research and Educationalvaluable addition to the diagnostic tool kit. Another
Foundation, and other private institutions.NINDS-funded study focuses on the development of
The ultimate hope for curing cerebral palsy rests withfetal magnetoencephalography (fMEG) - a technology
prevention. In order to prevent cerebral palsy,that would allow doctors to look for abnormalities in
however, scientists have to understand normal fetalfetal brain activity.
brain development so that they can understand whatEpidemiological studies - studies that look at the
happens when a baby's brain develops abnormally.distribution and causes of disease among people --
Between conception and the birth of a baby, one cellhelp scientists understand risk factors and outcomes
divides to form a handful of cells, and then hundreds,for particular diseases and medical conditions.
millions, and, eventually, billions of cells. Some of theseResearchers have established that preterm birth
cells specialize to become brain cells, and then(when a baby is born before 32 weeks' gestation) is
specialize even further into particular types ofthe highest risk factor for cerebral palsy.
neurons that travel to their appropriate place in theConsequently, the increasing rate of premature births
brain (a process that scientists call neuronal migration).in the United States puts more babies at risk. A large,
Once they are in the right place, they establishlong-term study funded by the NIH is following a
connections with other brain cells. This is how thegroup of more than 400 mothers and their infants
brain develops and becomes able to communicateborn between 24 and 31 weeks' gestation. They are
with the rest of the body -- through overlappinglooking for relationships between preterm birth,
neural circuits made up of billions of interconnectedmaternal uterine infection, fetal exposure to infection,
and interdependent neurons.and short-term and long-term health and neurological
Many scientists now think that a significant number ofoutcomes. The researchers are hoping to discover
children develop cerebral palsy because of mishapsenvironmental or lifestyle factors, or particular
early in brain development. They are examining howcharacteristics of mothers, which might protect
brain cells specialize and form the right connections,preterm babies from neurological disabilities.
and they are looking for ways to prevent theWhile this research offers hope for preventing
factors that disrupt the normal processes of braincerebral palsy in the future, ongoing research to
development.improve treatment brightens the outlook for those
Genetic defects are sometimes responsible for thewho must face the challenges of cerebral palsy
brain malformations and abnormalities that causetoday. An important thrust of such research is the
cerebral palsy. Scientists funded by the NINDS areevaluation of treatments already in use so that
searching for the genes responsible for thesephysicians and parents have valid information to help
abnormalities by collecting DNA samples from peoplethem choose the best therapy. A good example of
with cerebral palsy and their families and using geneticthis effort is an ongoing NINDS-supported study that
screening techniques to discover linkages betweenpromises to yield new information about which
individual genes and specific types of abnormality -patients are most likely to benefit from selective
primarily those associated with abnormal neuronaldorsal rhizotomy, a surgical technique that is
migration.increasingly being used to reduce spasticity (see
Scientists are scrutinizing events in newborn babies'Surgery).
brains, such as bleeding, epileptic seizures, andSimilarly, although physical therapy programs are used
breathing and circulation problems, which can causealmost universally to rehabilitate children with cerebral
the abnormal release of chemicals that trigger thepalsy, there are no definitive studies to indicate which
kind of damage that causes cerebral palsy. Fortechniques work best. For example,
example, research has shown that bleeding in theconstraint-induced therapy (CIT) is a type of physical
brain unleashes dangerously high amounts of a braintherapy that has been used successfully with adult
chemical called glutamate. Although glutamate isstroke survivors and individuals who have traumatic
necessary in the brain to help neurons communicate,brain injury and are left with a weak or disabled arm
too much glutamate overexcites and kills neurons.on one side of the body. The therapy involves
Scientists are now looking closely at glutamate torestraining the stronger arm in a cast and forcing the
detect how its release harms brain tissue. By learningweaker arm to perform 6 hours of intensive
how brain chemicals that are normally helpful become"shaping" activities every day over the course of 3
dangerously toxic, scientists will have opportunities toweeks. The researchers who conducted the clinical
develop new drugs to block their harmful effects.trials in adult stroke survivors realized CIT's potential
Scientists funded by the NINDS are also investigatingfor strengthening children's arms weakened by
whether substances in the brain that protect neuronscerebral palsy.
from damage, called neurotrophins, could be used toIn a randomized, controlled study of children with
prevent brain damage as a result of stroke orcerebral palsy funded by the NIH, researchers put
oxygen deprivation. Understanding how theseone group of children through conventional physical
neuroprotective substances act would allow scientiststherapy and another group through 21 consecutive
to develop synthetic neurotrophins that could bedays of CIT. Researchers looked for evidence of
given immediately after injury to prevent neuronimprovement in the movement and function of the
death and damage.disabled arm, whether the improvement lasted after
The relationship between uterine infections duringthe end of treatment, and if it was associated with
pregnancy and the risk of cerebral palsy continues tosignificant gains in other areas, such as trunk control,
be studied by researchers funded by the NIH. Theremobility, communication, and self-help skills.
is evidence that uterine infections trigger inflammationChildren receiving CIT outperformed the children
and the production of immune system cells calledreceiving conventional physical therapy across all
cytokines, which can pass into an unborn baby's brainmeasures of success, including how well they could
and interrupt normal development. By understandingmove their arms after therapy and their ability to do
what cytokines do in the fetal brain and the type ofnew tasks during the study and then at home with
damage these immune system cells cause,their families. Six months later they still had better
researchers have the potential to developcontrol of their arm. The results from this study are
medications that could be given to mothers withthe first to prove the benefits of a physical therapy.
uterine infections to prevent brain damage in theirAdditional research to determine the optimal length
unborn children.and intensity of CIT will allow doctors to add this
Approximately 10 percent of newborns are borntherapy to the cerebral palsy treatment toolbox.
prematurely, and of those babies, more than 10Studies have shown that functional electrical
percent will have brain injuries that will lead tostimulation is an effective way to target and
cerebral palsy and other brain-based disabilities. Astrengthen spastic muscles, but the method of
particular type of damage to the white matter of thedelivering the electrical pulses requires expensive,
brain, called periventricular leukomalacia (PVL), is thebulky devices implanted by a surgeon, or skin surface
predominant form of brain injury in premature infants.stimulation applied by a trained therapist.
NINDS-sponsored researchers studying PVL areNINDS-funded researchers have developed a
looking for new strategies to prevent this kind ofhigh-tech method that does away with the bulky
damage by developing safe, nontoxic therapiesapparatus and lead wires by using a hypodermic
delivered to at-risk mothers to protect their unbornneedle to inject microscopic wireless devices into
babies.specific muscles or nerves. The devices are powered
Although congenital cerebral palsy is a condition thatby a telemetry wand that can direct the number and
is present at birth, a year or two can pass beforestrength of their pulses by remote control. The
any disabilities are noticed. Researchers have showndevice has been used to activate and strengthen
that the earlier rehabilitative treatment begins, themuscles in the hand, shoulder, and ankle in people
better the outcome for children with cerebral palsy.with cerebral palsy as well as in stroke survivors.
But an early diagnosis is hampered by the lack ofAs researchers continue to explore new treatments
diagnostic techniques to identify brain damage orfor cerebral palsy and to expand our knowledge of
abnormalities in infants.brain development, we can expect significant
Research funded by the NINDS is using imagingimprovements in the care of children with cerebral
techniques, devices that measure electrical activity inpalsy and many other disorders that strike in early
the brain, and neurobehavioral tests to predict thoselife.